Pulmonary Stenosis Jeffrey D Dayton, Ralf J Holzer, Robert H Anderson Abstract This chapter discusses pulmonary stenosis as an isolated finding Where pulmonary stenosis exists as part of a more complex anomaly, such as tetralogy of Fallot, the reader is directed to the complete descriptions found in the relevant chapters Keywords Pulmonary valve stenosis; congenital heart disease; pulmonary valvuloplasty This chapter discusses pulmonary stenosis as an isolated finding When pulmonary stenosis exists as part of a more complex anomaly, such as tetralogy of Fallot, the reader is directed to the complete descriptions found in the relevant chapters Incidence and Associated Anomalies Pulmonary stenosis is the third most common congenital cardiac malformation In a large prospective study of all live-born infants that also included data from the autopsies of stillborn infants,1 the total incidence of congenitally malformed hearts was 6.6 per 1000 live births Of these, pulmonary stenosis accounted for 5.8% Half of all congenitally malformed hearts include pulmonary stenosis as a component of the defect