what causes sickle cell disease

... participants as par prevention of sickle cell disease and attitude towards their children with sickle cell disease Table 4: Participants’ knowledge about causes of sickle cell disease and attitudes towards ... about the cause(s) of sickle cell disease and the attitude of parents towards their children with sickle cell disease Hypothesis 4: Knowledge of the impact of sickle cell disease will not make ... about the cause(s) of sickle cell disease of the participants and their attitude towards their children with sickle cell disease Knowledge of the impact of sickle cell disease will not make significant...

Ngày tải lên: 12/02/2014, 19:20

... children with sickle cell disease Journal of Pediatrics, 145, 622-627 Center for Disease Control (2010) Sickle Cell Disease: Data and Statistics Retrieved from http://www.cdc.gov/ncbddd/sicklecell/data.html ... outcomes in young children with sickle cell disease Journal of Pediatrics, 145, 99-106 Silva, C M., & Viana, M B (2002) Growth deficits in children with sickle cell disease Archives of Medical Research, ... Hoppe, C., Telen, M J.; Investigators, Comprehensive Sickle Cell Centers (2010) Definitions of the phenotypic manifestations of sickle cell disease American Journal of Hematology, 85, 6-13 Buison,...

Ngày tải lên: 12/02/2014, 19:20

... within the definition of SCD: homozygous sickle cell (SS) disease, sickle haemoglobin C (SC) disease, sickle cell bz thalassaemia (S bz thalassaemia) and sickle cell b0 thalassaemia (S b0 thalassaemia).7 ... patterns of children with sickle- cell disease Hum Biol 1976; 48:429–37 25 Booker CR, Scott RB, Ferguson AD Studies in sickle cell anaemia Xxii Clinical manifestations of sickle cell anaemia during ... homozygous sickle cell disease Hum Biol 1977; 49:429–36 12 Singhal A, Morris J, Thomas P, Dover G, Higgs D, Serjeant G Factors affecting prepubertal growth in homozygous sickle cell disease Arch...

Ngày tải lên: 12/02/2014, 19:20

... βs Sickle cell disease- SS SCD-SS βs / βc Sickle cell disease- SC SCD-SC βs / / βo thalassemia βs / β+ thalassemia thalassemia SCD-S βo thal Sickle cell disease- S β+ thalassemia SCD-S β+ thal Sickle ... Sickle cell disease- S βo DIAGNOSIS AND COUNSELING W ORLD W IDE W EB R ESOURCES SICKLE CELL AND GENETIC WEB SITES Sickle Cell Disease Association of America (SCDAA) http://www.sicklecelldisease.org ... Development Sickle Cell Disease Association of America P.O Box 1956 Baltimore, MD 21203 Tel: (410) 363-7711 Fax: (410) 363-4052 E-mail: siross@sicklecelldisease.org Ms Kathy Norcott Sickle Cell Disease...

Ngày tải lên: 21/02/2014, 12:20

... Introduction Sickle Cell Disease Sickle cell disease is a genetic disorder that decreases life expectancy by 25 to 30 years and affects approximately 80,000 Americans.1,2 Sickle cell disease refers ... use of hydroxyurea for sickle cell disease The dosing of hydroxyurea for sickle cell disease is comparable to that in other diseases, although in the case of malignant disease, more drug is often ... toxicities in sickle cell disease We excluded trials involving other diseases if fewer than 20 patients received hydroxyurea We allowed cohort studies of diseases other than sickle cell disease only...

Ngày tải lên: 05/03/2014, 10:20

... Children with Sickle Cell Disease Pediatrics 2002 Mar;109 (3): 526-35 Steinberg MH, Management of Sickle Cell Disease NEJM 1999 Apr; 340 (13): 1021-30 Fixler J, Styles L Sickle Cell Disease Pediatr ... date Inclusion Criteria: Children with sickle cell disease and a fever as defined by an oral temperature of > 38 ºC CPG 21-1 Management of Sickle Cell Disease in Children Page of 15 Assessment ... with the use of the pre printed physician order Paediatric Sickle Cell Disease References: Child Health Network: Management of Sickle Cell Disease in Children Practice Guideline 20042004 Vichinsky...

Ngày tải lên: 05/03/2014, 12:20

... with sickle cell disease: a report from the Cooperative Study of Sickle Cell Disease Journal of Pediatrics, 139, 391–397 Whitten, C.F & Fischoff, J (1974) Psychosocial effects of sickle cell disease ... M., Knight & J.M (1998) Management of sickle cell disease (Letters) British Medical Journal, 316, 935 Alao, A.O & Cooley, E (2001) Depression and sickle cell disease Harvard Review of Psychiatry, ... utilisation in a UK study of paediatric sickle cell pain Archives of Disease in Childhood, 86, 325–329 Anie, K.A.; Steptoe, A & Bevan, D.H (2002b) Sickle cell disease: pain, coping, and quality of...

Ngày tải lên: 14/03/2014, 11:20

... 1) sickle cell disease without co-morbidities (n = 47), 2) sickle cell disease with neurobehavioral co-morbidities (n = 23), 3) sickle cell disease with medical co-morbidities (n = 12), 4) sickle ... children with and without sickle cell disease In addition, we also compared parents of children with sickle cell disease to parents of children without sickle cell disease and without other co-morbidities ... with severe sickle cell disease reported significantly worse scores in the communication and worry scales than children with mild sickle cell disease and children without sickle cell disease In...

Ngày tải lên: 18/06/2014, 18:20

... D: Depression, disease severity, and sickle cell disease J Behav Med 1999, 22(2):115-126 Ohaeri JU, Shokunbi WA, Akinlade KS, Dare LO: The psychosocial problems of sickle cell disease sufferers ... adults with sickle cell disease J Natl Black Nurses Assoc 2001, 12(2):36-43 Kater AP, Heijboer H, Peters M, Vogels T, Prins MH, Heymans HS: [Quality of life in children with sickle cell disease in ... sickle cell disease and its impact on quality of life: Qualitative findings from focus groups Br J Health Psychol 2002, 7(Part 3):345-363 Anie KA: Psychological complications in sickle cell disease...

Ngày tải lên: 18/06/2014, 19:20

... youngsters with sickle cell disease Child Dev 1996, 67(2):423-436 Barakat LP, Lash LA, Lutz MJ, Nicolaou DC: Psychosocial Adaptation of Children and Adolescents With Sickle Cell Disease In Comprehensive ... coping in sickle cell disease Arch Dis Child 1996, 75(3):199-203 Panepinto JA, O'Mahar KM, DeBaun MR, Loberiza FR, Scott JP: Health-related quality of life in children with sickle cell disease: ... quality of life in children with sickle cell disease J Behav Med 2002, 25(3):269-283 Thomas VJ, Taylor L: The psychosocial experience of people with sickle cell disease and its impact on quality...

Ngày tải lên: 18/06/2014, 19:20

... Homozygote sickle cell disease in patients above 20 years of age: follow-up of patients in Dakar Rev Med Interne 2003, 24:711-715 25 Platt OS, Brambilla DJ, Rosse WF: Mortality in sickle cell disease, ... outcomes in patients with sickle cell disease and frequent vaso-occlusive crises Am J Med Sci 2003, 325:107-109 27 Yetunde A, Anyaegbu CC: Profile of the Nigerian sickle cell anaemia patients above ... Osteonecrosis of the hip in sickle cell haemoglobinopathy The Am J Orthop 1995, 1:18-24 33 Okany CC, Akinyanju OO: The influence of socio-economic Status on the severity of sickle cell disease Afr J Med...

Ngày tải lên: 20/06/2014, 04:20

... Published: 26 October 2010 References Stuart MJ, Nagel RL: Sickle- cell disease Lancet 2004, 364:1343-1360 Roberts I, de Montalembert M: Sickle cell disease as a paradigm of immigration hematology: new ... complications in sickle cell disease Br J Haematol 2005, 129:723-729 Barakat L, Lash LA, Lutz MJ, Nicolaou DC: Psychosocial Adaptation of Children and Adolescents with Sickle Cell Disease In Comprehensive ... with sickle cell disease Child Dev 1996, 67:423-436 Noll RB, Reiter-Purtill J, Vannatta K, Gerhardt CA, Short A: Peer relationships and emotional well-being of children with sickle cell disease: ...

Ngày tải lên: 20/06/2014, 15:20

... D: Depression, disease severity, and sickle cell disease J Behav Med 1999, 22(2):115-126 Ohaeri JU, Shokunbi WA, Akinlade KS, Dare LO: The psychosocial problems of sickle cell disease sufferers ... adults with sickle cell disease J Natl Black Nurses Assoc 2001, 12(2):36-43 Kater AP, Heijboer H, Peters M, Vogels T, Prins MH, Heymans HS: [Quality of life in children with sickle cell disease in ... sickle cell disease and its impact on quality of life: Qualitative findings from focus groups Br J Health Psychol 2002, 7(Part 3):345-363 Anie KA: Psychological complications in sickle cell disease...

Ngày tải lên: 20/06/2014, 16:20

... poststreptococcal glomerulonephritis; RF: rheumatoid factor; SCA: sickle cell anemia; SCD: sickle cell disease; SCN: sickle cell nephropathy; VDRL: Venereal Disease Research Laboratory Author details Department ... Wilkinson AH, Lew SQ: Renal abnormalities in sickle cell disease Kidney Int 2000, 57:1-8 Ataga KI, Orringer EP: Renal abnormalities in sickle cell disease Am J Hematol 2000, 63(Suppl 4):205-211 ... year, but she was lost to follow-up Discussion Sickle cell nephropathy (SCN) is an important cause of mortality and morbidity in patients with SCD Sickle cell anemia (SCA) and the related hemoglobinopathies...

Ngày tải lên: 11/08/2014, 00:22

... management of sickle cell disease N Engl J Med 1995, 333:206-213 Koshy M, Weiner SJ, Miller , Sleeper AL, Vichinsky EP, Brown AK, Khakoo Y, Kinney TR: Surgery and anaesthesia in sickle cell disease ... hemoglobin SC disease: preoperative transfusion in sickle cell disease study group Am J Hematol 1998, 57:101-108 12 Haberkern C, Neumayr L, Orringer EP: Cholecystectomy in sickle cell anemia patients: ... transfusion in sickle cell disease study group Blood 1997, 89:1533-1542 13 Ritterbach C, Burkle H, Durken M, Wappler F: Anesthesiological management in patients with sickle cell disease Anesthesiol...

Ngày tải lên: 11/08/2014, 12:20

... children with homozygous sickle cell (SS) disease, 178 with sickle cell- haemoglobin C (SC) disease, 33 with sickle cell- beta + thalassaemia (S beta+ thal) and 14 with sickle cellbeta0 thalassaemias ... Published: June 2010 References Serjeant G, Serjeant B: Nomenclature and genetics of Sickle Cell Disease Sickle Cell Disease Oxford: Oxford University PressSerjeant G, Serjeant B , 2001, 31-40 Nesse ... Lawson W, Castro O: Depression in sickle cell disease J Natl Med Assoc 2003, 95:533-537 Molock SD, Belgrave FZ: Depression and anxiety in patients with sickle cell disease: conceptual and methodological...

Ngày tải lên: 11/08/2014, 16:22

... patients with homozygous sickle cell disease Eur J Clin Nutr 1989, 43:609-614 63 Houston PE, Rana S, Sekhsaria S, Perlin E, Kim KS, Castro OL: Homocysteine in sickle cell disease: relationship to ... Jain SK, Shohet SB: A novel phospholipid in irreversibly sickled cells: evidence for in vivo peroxidative membrane damage in sickle cell disease Blood 1984, 63:362-367 Hebbel RP, Eaton JW, Balasingam ... formation and apoptosis in transgenic sickle cell mouse kidneys Kidney Int 1998, 54: 1520-1528 Aslan M, Thornley-Brown D, Freeman BA: Reactive species in sickle cell disease Ann NY Acad Sci 2000, 899:375-391...

Ngày tải lên: 12/08/2014, 18:20

... patients with concomitant asthma and sickle cell disease Table 2: Results in children with sickle cell disease with and without asthma Patients with Sickle Cell & Asthma (n = 48) Admissions for ... Daeschner C, Manci E: Causes and Outcomes of the Acute Chest Syndrome in Sickle Cell Disease N Engl J Med 2000, 342:1855-1865 Quinn C, Buchanan G: The acute chest syndrome of sickle cell disease J Pediatr ... control group of 48 children with sickle cell disease alone The 48 children with sickle cell and asthma represented all patients with complete medical records with both diseases that were cared for...

Ngày tải lên: 13/08/2014, 13:22

... sickle cell anemia (SCA) (Hb SS), sickle cell hemoglobin C disease (Hb SC) and sickle cell B thalassaemia (SB Thal.) and the condition is characterized by red blood cell sickling patho-physiology ... age of twelve Sickle cell disease (SCD) is found prevalent in black race, Arabians and the Caribbean [1] It is a hereditary and chronic medical condition that encompasses sickle cell anemia (SCA) ... 85:267-276 Morin C, Warin EM: Depression and sickle cell anemia South Med J 1981, 74:766-768 Iloeje SO: Psychiatric morbidity among children with sickle cell disease Dev Med Child Neurol 1991, 33(12):1087-94...

Ngày tải lên: 13/08/2014, 18:21

... of his condition (i.e., sickle cell anemia or SS disease, sickle C disease or SC disease, sickle beta thalassemia disease or S beta thal disease, etc.) He should know what kinds of medicines ... Guidelines for Parents See Appendices A and B for answers to the questions What is Sickle Cell Disease? ” and What Causes Sickle Cell Disease? ” Prevent Problems Build Self-Esteem The best way to help ... child with sickle cell disease It can be helpful to teach all of your children about sickle cell disease If they have questions that you can’t answer, let them ask the staff at the sickle cell center...

Ngày tải lên: 12/02/2014, 12:20