... study is limited in its abilityto demonstrate pulmonary vascular anatomy and collat-eral arterial supply [10].Angiography remains the gold standard for the diagnosis of pulmonary artery agenesis. ... response.DiscussionCongenital UAPA is a rare anomaly that may occur inisolation but most frequently is accompanied by cardio-vascular malformations such as tetralogy of Fallot, septaldefects, patent ductus arteriosus, ... 2002,122:1471-1477.3. Shakibi JG, Rastan H, Nazarian I, Paydar M, Aryanpour I, Siassi B: Isolatedunilateral absence of the pulmonary artery: review of the worldliterature and guidelines for surgical repair. Jpn...