... Road,Cambridge CB2 2XY, UK.Fax: + 44 12 2 3 25 2905, Tel.: + 44 12 2 3 25 2900,E-mail: mpm@mrc-dunn.cam.ac.uk,http://www.mrc-dunn.cam.ac.ukAbbreviations: DC- 81, (11 aS)-8-hydroxy-7-methoxy -1 ,2, 3 ,11 a-tetrahydro-5H-pyrrolo [2, 1- c] [1, 4]benzodiazepin-5-one; ... retinitis pigmentosa; PNA, peptide nucleicacid; TPMP, methyl triphenylphosphonium; TPP, triphenyl-phosphonium.(Received 27 February 20 03, revised 15 April 20 03,accepted 12 May 20 03)Eur. ... mitoDC- 81, [4-( (11 aS)-7-methoxy -1 ,2, 3 ,11 a-tetrahydro-5H-pyrrolo [2, 1- c] [1, 4]benzodiazepin-5 -on- 8-oxy)butyl]tri-phenylphosphonium iodide; mtDNA, mitochondrial DNA; NARP,neuropathy, ataxia and...